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  1. Radiopaedia
    https://radiopaedia.org/articles/lymphangioleiomyomatosis-1

    Lymphangioleiomyomatosis | Radiology Reference Article

    • Lymphangioleiomyomatosis (LAM) is a low-grade destructive metastasizing PEComatous tumor 1 resulting from the proliferation of LAM cells in the lung, kidney and axial lymphatics. The di… Mehr anzeigen

    Epidemiology

    Symptomatic CLD almost exclusively affects women and is associated with sporadic lymphangioleiomyomatosis (s-LAM) or tuberous sclerosis complex (TSC-LAM)… Mehr anzeigen

    Radiopaedia
    Clinical Presentation

    s-LAM can present in late teens or adulthood with lymphatic or lung disease. TSC-LAM … Mehr anzeigen

    Radiopaedia
    Diagnosis

    American Thoracic Society/Japanese Respiratory Society guidelines 2017 2 support a clinical diagnosis of LAM based on typical lung CT and accompanied by any of the … Mehr anzeigen

    Radiopaedia
    Pathology

    Smooth muscle-like LAM cells contain inactivating mutations of TSC2 or TSC1tumor suppressor genes with consequent activation of the mechanistic target … Mehr anzeigen

    Radiopaedia
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  1. Radiopaedia
    https://radiopaedia.org/articles/lymphangioleiomyomatosis-diagnosti…

    Lymphangioleiomyomatosis diagnostic criteria (mnemonic)

    Erkunden Sie weiter

    Imaging Features of Lymphangioleiomyomatosis: …
    ajronline.org
    CT Grading of Lung Disease in …
    ajronline.org
    Empfohlen auf der Grundlage der beliebten • Feedback
  2. Radiopaedia
    https://images.radiopaedia.org/cases/lymphangioleiomyomatosis-22

    Lymphangioleiomyomatosis | Radiology Case | Radiopaedia.org

  3. MDS Manuals
    https://www.msdmanuals.com/de-de/profi/lungenkrankheiten/interstiti...

    Lymphangioleiomyomatose - Lungenkrankheiten - MSD Manual …

  4. DocCheck Flexikon
    https://flexikon.doccheck.com/de/Lymphangioleiomyomatose

    Lymphangioleiomyomatose - DocCheck Flexikon

  5. European Respiratory Society
    https://erj.ersjournals.com/content/35/1/14

    European Respiratory Society guidelines for the …

    WEBLymphangioleiomyomatosis (LAM) is a rare lung disease, which occurs sporadically or in association with the genetic disease tuberous sclerosis complex (TSC) 1, 2. Sporadic LAM affects ∼1 in 400,000 adult females; …

  6. Ähnliche Fragen
    What is Lam disease?
    LAM is a complex disorder where the pathophysiology is only partially understood, with increasing knowledge emerging as to the underlying molecular drivers of disease.

    Lymphangioleiomyomatosis: a clinical review - European Respiratory So…

    breathe.ersjournals.com
    What is sporadic Lam (Lam)?
    Sporadic LAM affects ∼1 in 400,000 adult females; in TSC, LAM occurs in 30–40% of adult females 3, 4 and exceptionally in males and children 5, 6. Patients with LAM usually develop progressive dyspnoea and recurrent pneumothorax, chylous collections and occasional haemoptysis 1.

    European Respiratory Society guidelines for the diagnosis and manage…

    erj.ersjournals.com
    What is lymphangioleiomyomatosis (LAM)?
    Lymphangioleiomyomatosis (LAM) is a low-grade destructive metastasizing PEComatous tumor 1 resulting from the proliferation of LAM cells in the lung, kidney and axial lymphatics. The disease is caused by mutations of the TSC2 or TSC1 genes and is more commonly sporadic rather than inherited.

    Lymphangioleiomyomatosis | Radiology Reference Article | Radiopaedia…

    radiopaedia.org
    How can a patient group help with the diagnosis of Lam?
    The diagnosis of an orphan disease and its consequences often leave patients with a feeling of isolation. Patient groups can help with these issues and other practical matters. LAM is associated with an increased risk of pneumothorax which occurs in ∼40% of patients at presentation and 66% of patients during the course of the disease 10, 55.

    European Respiratory Society guidelines for the diagnosis and manage…

    erj.ersjournals.com
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  7. Lungeninformationsdienst
    https://www.lungeninformationsdienst.de/krankheiten/weitere...

    Lymphangioleiomyomatose (LAM) - Lungeninformationsdienst

  8. European Respiratory Society
    https://breathe.ersjournals.com/content/…

    Lymphangioleiomyomatosis: a clinical review

    WEBLymphangioleiomyomatosis (LAM) is a diffuse cystic lung disease. There are two main types of LAM: sporadic, and LAM associated with the tuberous sclerosis complex (TSC), which is caused by mutations in the …

  9. RSNA Publications Online
    https://pubs.rsna.org/doi/full/10.1148/rg.253…

    Lymphangioleiomyomatosis: Radiologic-Pathologic …

    WEB1. Mai 2005 · Lymphangioleiomyomatosis (LAM) is an uncommon interstitial lung disease that exclusively affects women, usually during their reproductive years. LAM is characterized pathologically by abnormal …

  10. Lungeninformationsdienst
    https://www.lungeninformationsdienst.de/krankheiten/weitere...

    Lymphangioleiomyomatose (LAM): Symptome und Grundlagen ...

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